Document Type : Case Report

Authors

1 Rheumatology Department, Shahid Sadoughi University of Medical Sciences, Yazd, Iran

2 Division of Radiology, Shahid Sadoughi University of Medical Sciences, Yazd, Iran

3 Division of Rheumatology, Shahid Sadoughi University of Medical Sciences, Yazd, Iran

Abstract

Hemophagocytic lymphohistiocytosis in a patient with systemic lupus erythematous

Abstract

Hemophagocytic lymphohistiocytosis (HLH), is a disorder seen more often in children and is life-threatening due to by over- activation of macrophages and T cells resulting in cytokine storm. HLH can be familial or secondary to infections, malignancy, immunosuppression, and autoimmune conditions such as SLE. We report a 10-year old female with previously diagnosed SLE who hospitalized because of fever and pancytopenia.

Key words: SLE, HLH, Cytokine storm, pancytopenia

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